Alport syndrome is an oculo-renal syndrome characterized by a triad of clinical findings consisting of hemorrhagic nephritis, sensorineural hearing loss and characteristic ocular findings.
The triad of Alport syndrome is SNHL – Sensorineural deafness, Progressive kidney failure and Ocular anomalies. Remember the mnemonic KOH to remember the triad of Alport syndrome.
K – Kidney : Hemorrhagic nephritis
0 – Ocular anomalies
H – Hearing deficit : SNHL
Among ocular signs, anterior lenticonus and dot fleck retinopathy are the classic ocular anomalies described in Alport syndrome.