Triad of Alport Syndrome

Alport syndrome is an oculo-renal syndrome characterized by a triad of clinical findings consisting of hemorrhagic nephritis, sensorineural hearing loss and characteristic ocular findings.

The triad of Alport syndrome is SNHL – Sensorineural deafness, Progressive kidney failure and Ocular anomalies. Remember the mnemonic KOH to remember the triad of Alport syndrome.

K – Kidney : Hemorrhagic nephritis

0 – Ocular anomalies

H – Hearing deficit : SNHL

Among ocular signs, anterior lenticonus and dot fleck retinopathy are the classic ocular anomalies described in Alport syndrome.

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